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MYOCLONIC ASTATIC EPILEPSY (DOOSE SYNDROME)

https://doi.org/10.17650/2073-8803-2013-8-1-25-38

Abstract

The authors proposed a detailed review of literature devoted to myoclonic astatic epilepsy (Doose syndrome). The authors describe the history of study of myoclonic astatic epilepsy, its prevalence, etiology and the role of genetic factors, clinical pictures, including the main type of seizures, diagnostic criteria and nosology. The characteristics of EEG and neuroimaging are prescribed, and also differential diagnosis, approaches to treatment and prognosis.

About the Authors

K. Yu. Mukhin
Институт детской неврологии и эпилепсии им. Святителя Луки
Russian Federation
Москва


M. B. Mironov
Институт детской неврологии и эпилепсии им. Святителя Луки
Russian Federation
Москва


O. A. Pylaeva
Институт детской неврологии и эпилепсии им. Святителя Луки
Russian Federation
Москва


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For citations:


Mukhin K.Yu., Mironov M.B., Pylaeva O.A. MYOCLONIC ASTATIC EPILEPSY (DOOSE SYNDROME). Russian Journal of Child Neurology. 2013;8(1):25-38. (In Russ.) https://doi.org/10.17650/2073-8803-2013-8-1-25-38

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