Idiopathic autoimmune encephalitis with a recurrent course. A case report
https://doi.org/10.17650/2073-8803-2023-18-1-52-56
Abstract
We presented a clinical case of idiopathic autoimmune brainstem encephalitis in a 12-year-old female patient. At the onset of the disease, which developed after a respiratory infection, the clinical picture was accompanied by oculomotor and bulbar syndromes. The diagnosis of Bickerstaff brainstem encephalitis was made based on clinical diagnostic criteria and the positive effect of the course of intravenous immunoglobulin therapy. During 3 years of follow-up, there were periods of relapse of the disease, during which symptoms not typical for Bickerstaff stem encephalitis appeared. Against the background of long-term immunosuppressive therapy, there was a long-term remission of about 2 years. The clinical picture, the presence of relapses, the data of additional methods forced to reconsider the diagnosis in favor of idiopathic autoimmune brainstem encephalitis.
About the Authors
A. B. Davletova
City Polyclinic № 219 of the Moscow Health Department
Russian Federation
Russian Federation
10/2 Rodionovskaya St., Moscow 123466
A. Yu. Ryabchenko
Orenburg State Medical University, Ministry of Health of Russia
Russian Federation
Russian Federation
Аleksandr Yuryevich Ryabchenko
Sovetskaya St., Orenburg 460000
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Review
For citations:
Davletova A.B., Ryabchenko A.Yu. Idiopathic autoimmune encephalitis with a recurrent course. A case report. Russian Journal of Child Neurology. 2023;18(1):52-56. (In Russ.) https://doi.org/10.17650/2073-8803-2023-18-1-52-56
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