RESISTANT EPILEPSY FORMS, ASSOCIATED WITH FEVER-PROVOKED (FEBRILE) EPILEPTIC SEIZURES (DRAVET SYNDROME, DESC, HHE) (A LECTURE)
https://doi.org/10.17650/2073-8803-2012-7-4-31-40
Abstract
The most important characteristics of resistant epilepsy forms, associated with fever-provoked (febrile) epileptic seizures (Dravet syndrome, DESC — Devastating epileptic encephalopathy in school-aged children, HHE — hemiconvul- sion-hemiplegia-epilepsy syndrome) are proposed. For every syndrome all the main aspects of disease are considered in detail: aetiology and pathogenesis, clinical picture, including of characteristics of seizures, EEG, neuroimaging, therapeutic approachers and prognosis.
About the Author
M. Yu. Bobylova
Институт, детской неврологии и эпилепсии им. Святителя Луки
Russian Federation
Russian Federation
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Review
For citations:
Bobylova M.Yu. RESISTANT EPILEPSY FORMS, ASSOCIATED WITH FEVER-PROVOKED (FEBRILE) EPILEPTIC SEIZURES (DRAVET SYNDROME, DESC, HHE) (A LECTURE). Russian Journal of Child Neurology. 2012;7(4):31-40. (In Russ.) https://doi.org/10.17650/2073-8803-2012-7-4-31-40
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