HEMICONVULSION-HEMIPLEGIA-EPILEPSY SYNDROME (HHE SYNDROME) (A LECTURE)
https://doi.org/10.17650/2073-8803-2012-7-4-17-30
Abstract
Hemiconvulsion-hemiplegia-epilepsy syndrome (HHE syndrome) — polyetiologic disease, with onset in childhood, characterized by the triad of symptoms: 1) prolonged convulsive seizures (usually on background of fever), involving one half of the body (hemiconvulsions); 2) acute hemiparesis occurring immediately after seizures (on the side of convulsions); 3) symptomatic focal epilepsy, occurring in the sequel. The authors discuss in detail different aspects of the disease, including etiology, pathogenesis, diagnostic approaches, differential diagnosis, and approaches to treatment (including prevention and therapy of the disease) and outcome.
About the Authors
K. Yu. Mukhin
Институт детской неврологии и эпилепсии имени Святителя Луки (Москва)
Russian Federation
Russian Federation
M. Yu. Bobylova
Институт детской неврологии и эпилепсии имени Святителя Луки (Москва)
Russian Federation
Russian Federation
A. F. Dolinina
Челябинская областная детская клиническая больница
Russian Federation
Russian Federation
O. A. Pylaeva
Институт детской неврологии и эпилепсии имени Святителя Луки (Москва)
Russian Federation
Russian Federation
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Review
For citations:
Mukhin K.Yu., Bobylova M.Yu., Dolinina A.F., Pylaeva O.A. HEMICONVULSION-HEMIPLEGIA-EPILEPSY SYNDROME (HHE SYNDROME) (A LECTURE). Russian Journal of Child Neurology. 2012;7(4):17-30. (In Russ.) https://doi.org/10.17650/2073-8803-2012-7-4-17-30
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