Russian Journal of Child NeurologyRussian Journal of Child NeurologyРусский журнал детской неврологии2073-88032412-9178Publishing House ABV Press40710.17650/2073-8803-2022-17-3-63-71REVIEWS AND LECTURESОБЗОРЫ И ЛЕКЦИИMalformations of the cerebral cortex and epilepsy. Clinical lectureПороки развития коры головного мозга и эпилепсия. Клиническая лекцияhttps://orcid.org/0000-0001-6260-6989KotovA. S.КотовА. С.
Russian Federation

Alexey Sergeevich Kotov

61/2 Shchepkina St., Moscow 129110

Алексей Сергеевич Котов 

129110 Москва, ул. Щепкина, 61/2

alexeykotov1980@gmail.comhttps://orcid.org/0000-0002-3291-7994FirsovK. V.ФирсовК. В.
Russian Federation

61/2 Shchepkina St., Moscow 129110

129110 Москва, ул. Щепкина, 61/2

M.F. Vladimirsky Moscow Regional Research Clinical InstituteГБУЗ МО «Московский областной научно-исследовательский клинический институт им. М.Ф. Владимирского»1507202217363711712202217122022Copyright ©; 2022, ABV-PressCopyright ©; 2022, АБВ-пресс2022ABV-PressАБВ-прессhttps://rjdn.abvpress.ru/jour/about/editorialPolicieshttps://rjdn.abvpress.ru/jour/article/view/407

Malformations of the cerebral cortex are often the causes of epilepsy. The latest changes in their classification are summarized. The description of lissencephaly and Miller–Dicker syndrome, pachygyria, polymicrogyria, hemimegaloencephaly, holoprosencephaly, schizencephaly, gray matter heterotopia is given. The features of epilepsy in these diseases are described. Magnetic resonance imaging scans for focal cortical dysplasia, polymicrogyria, and gray matter heterotopia are presented.

Пороки развития коры головного мозга часто являются причинами эпилепсии. В рамках данной клинической лекции обобщены последние изменения в классификации пороков развития коры головного мозга, представлено описание лиссэнцефалии и синдрома Миллера–Дикера, пахигирии, полимикрогирии, гемимегалэнцефалии, голопрозэнцефалии, шизэнцефалии, гетеротопии серого вещества. Описаны особенности эпилепсии при данных заболеваниях. Представлены данные магнитно-резонансной томографии при фокальной кортикальной дисплазии, полимикрогирии, гетеротопии серого вещества.

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